Frontiers Lysosomal and Mitochondrial Liaisons in Niemann-Pick
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Last updated 08 abril 2025


Intracellular Cholesterol Trafficking and Impact in Neurodegeneration. - Abstract - Europe PMC

Frontiers Lysosomal and Mitochondrial Liaisons in Niemann-Pick Disease

IJMS, Free Full-Text

Niemann-Pick type C2 deficiency impairs autophagy-lysosomal activity, mitochondrial function, and TLR signaling in adipocytes - ScienceDirect

Mitochondrial biogenesis is transcriptionally repressed in lysosomal lipid storage diseases

Mitochondrial biogenesis is transcriptionally repressed in lysosomal lipid storage diseases

Mitochondrial biogenesis is transcriptionally repressed in lysosomal lipid storage diseases

Frontiers npc2-Deficient Zebrafish Reproduce Neurological and Inflammatory Symptoms of Niemann-Pick Type C Disease

Niemann-Pick type C2 deficiency impairs autophagy-lysosomal activity, mitochondrial function, and TLR signaling in adipocytes - ScienceDirect

Figures and data in Lysosomal cholesterol export reconstituted from fragments of Niemann-Pick C1

Adenosine A2A receptor stimulation restores cell functions and differentiation in Niemann-Pick type C-like oligodendrocytes
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